الفهرس 
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Abstract
Choledochal cysts are single or multiple dilatations of the extrahepatic biliary tree, intrahepatic biliary radicals, or both. They account for less than 1% of all benign biliary diseases with highest incidence in Asia especially in japan and in females.
They are classified according to Todani classification (1977) who classified them into 5 types, with types I and IV are the commonest and type V (Caroli’s disease) is the rarest.
The pathogenesis of choledochal cysts is multifactorial, mostly form distal bile duct obstruction (anatomical or functional) combined with raised intraductal pressure possibly from anomalous pancreatico-biliary duct junction.
High degree of clinical suspicion is required for diagnosis, as the classical triad of presentation is found only in 20% of cases (obstructive jaundice, right hypochondrial pain, and abdominal mass). Radiologically, Magnetic resonance cholangiopancreatography is the investigation of choice to evaluate such cases.
Surgery is the definitive treatment of choledochal cysts, with exception of type III. In general, all choledochal cysts should be excised with cholecystectomy and re-establishment of bile flow by biliary-enteric anastomosis. Laparoscopic cyst excision and hepaticojejunostomy for types I and II cysts is described as an alternative to open surgery.
Finally, long term postoperative follow up must be maintained because of age related risk of malignancy.