الفهرس 
Embryological and Surgical Anatomy of the liver, Intrahepaticand Extrahepatic Biliary TreeOnly 14 pages are availabe for public view
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Abstract
Biliary atresia (BA) is a progressive fibro-obliterative cholangiopathy of unclear etiology affecting varying degrees of both extra- and intrahepatic biliary tree resulting in obstructive bile flow and cholestasis in neonates. The diagnostic work-up is designed to diagnose or rule out BA without any unnecessary delay.
Biliary Atresia (BA) is the most common cause of chronic cholestasis in infants and the most frequent cause for surgery in cholestatic jaundice in this age group. It is a destructive inflammatory obliterative cholangiopathy that affects varying lengths of both intrahepatic and extrahepatic bile ducts if untreated, BA leads to cirrhosis, hepatic failure and death within the first two years of life. The overall survival rate after corrective surgery with Kasai portoenterostomy or liver transplantation when indicated is approximately 90%.