الفهرس | Only 14 pages are availabe for public view |
Abstract Bronchiectasis is a respiratory chronic condition characterized by cycles of impaired mucocilliary clearance, bronchial infection and inflammation resulting in irreversible airways dilatation. Cystic fibrosis is an autosomal recessive disease affects multiple system , its diagnosis requires clinical evidence and demonstration of CFTR dysfunction. Increased level of neutrophil elastase has been identified as a key risk factor for onset and progression of cystic fibrosis and non cystic fibrosis bronchiectasis. |