الفهرس 
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Abstract
Summary
Haemophilia is an X-linked heritable coagulopathy with an overall prevalence of approximately 1 in 10,000 individuals. The most common form is factor VIII deficiency, or haemophilia A, which comprises approximately 80% of cases. Factor IX deficiency, or haemophilia B, comprises approximately 20% of cases.
Other heritable clotting disorders include von Willebrand disease and various other clotting factor deficiencies, but these are not commonly classified as ‘haemophilia’. The aim of the present work was to evaluate hemophilic joints clinically, radiologically, and functionally in patients with hemophilic arthropathy.
This cross-sectional study was conducted on patients who are known hemophilic with previous attacks of joint bleeding that affected joint function.
This study conducted on 50 patients in Beni-Suef university hospital. This study revealed that both HJHS and Patterson scores were significantly higher in patients with attacks of spontaneous hemarthrosis than patients with only post traumatic hemarthrosis, only the FISH score was significantly higher in patients with age of presentation beyond the first six months of age, that there was no significant difference between patients with plasma transfusion and patients with no plasma transfusion regarding the three scores, there was no significant difference between patients with Cryoprecipitate transfusion and patients with no Cryoprecipitate transfusion regarding the three scores and age showed a significant positive correlation with Patterson score. Number of affected joints showed a significant negative correlation to FISH score and a significant positive correlation to HJHS. Frequency of hemarthrosis/month showed a significant positive correlation to HJHS.
The cryoprecipitate dose had a significant positive correlation to the Patterson score. The duration of cryoprecipitate transfusion showed significant positive correlations to both HJHS and Patterson scores. The frequency of factor transfusion / month showed a significant negative correlation to FISH score and a significant positive correlation to both HJHS and Patterson scores. There were significant negative correlations between the FISH score and the other two scores while there was a significant positive correlation between the HJHS and Patterson scores.