الفهرس | Only 14 pages are availabe for public view |
Abstract Proximal femoral focal deficiency (PFFD) is a congenital orthopedic condition involving the upper femur, adjacent soft tissues, and frequently, the acetabulum as well as distal portions of the limb. Although the disorder has not been thought to be genetic, some conclusions can be drawn from embryologic studies. Many classification was done fore this condition due to a wide spectrum of this abnormality, the recant one is Paley classification. Diagnosis and preoperative assessment were made depending upon clinical examination, x-rays, C.T. ,scanograms and MRI. Management of these cases represents a challenge for the orthopedic pediatric surgeon and the approach to management is based on a problem list for each patient. Due to the fact that, there are many variations of the cases, so, the treatment of these cases should be individualized with an aim to obtain leg length equalization at time of puberty and good function of the knees and hips. With the advent of Ilizarov system and technique, the need for amputation and prosthetic fitting which was followed in many cases of congenital femoral deficiency was not be the ideal management and attempts done for hip reconstruction, treatment of associated anomalies and lengthening had gained wide acceptance. With well planned treatment strategies and right choose of the patients. Cases of PFFD, could be managed correctly with a proper gain in length, stable Summary and conclusion functioning hips and knees and the need for amputations and prosthetic fitting will no longer be needed. |